Penicillamine‐induced lethal status dystonicus in a patient with Wilson's disease
Identifieur interne : 004728 ( Main/Exploration ); précédent : 004727; suivant : 004729Penicillamine‐induced lethal status dystonicus in a patient with Wilson's disease
Auteurs : Marina Svetel [Yougoslavie] ; Nadežda Šterni [Yougoslavie] ; Sanja Pejovi [Yougoslavie] ; Vladimir S. Kosti [Yougoslavie]Source :
- Movement Disorders [ 0885-3185 ] ; 2001-05.
Descripteurs français
- Pascal (Inist)
- Wicri :
- topic : Homme.
English descriptors
- KwdEn :
- Acute Kidney Injury (etiology), Adult, Case study, Chelating Agents (administration & dosage), Chelating Agents (adverse effects), Dystonia, Dystonia (chemically induced), Dystonia (complications), Enzymopathy, Fatal Outcome, Generalized, Hepatolenticular Degeneration (drug therapy), Human, Humans, Male, Penicillamine, Penicillamine (administration & dosage), Penicillamine (adverse effects), Rhabdomyolysis (etiology), Stiffness, Sulfur containing aminoacid, Syndrome, Toxicity, Wilson disease.
- MESH :
- chemical , administration & dosage : Chelating Agents, Penicillamine.
- chemical , adverse effects : Chelating Agents, Penicillamine.
- chemically induced : Dystonia.
- complications : Dystonia.
- drug therapy : Hepatolenticular Degeneration.
- etiology : Acute Kidney Injury, Rhabdomyolysis.
- Adult, Fatal Outcome, Humans, Male, Syndrome.
Abstract
A 37‐year‐old man with Wilson's disease is described, in whom the introduction of penicillamine therapy was followed after 3.5 weeks by the development of the status dystonicus with a fatal outcome.
Url:
DOI: 10.1002/mds.1111
Affiliations:
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Le document en format XML
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<term>Chelating Agents (adverse effects)</term>
<term>Dystonia</term>
<term>Dystonia (chemically induced)</term>
<term>Dystonia (complications)</term>
<term>Enzymopathy</term>
<term>Fatal Outcome</term>
<term>Generalized</term>
<term>Hepatolenticular Degeneration (drug therapy)</term>
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<term>Humans</term>
<term>Male</term>
<term>Penicillamine</term>
<term>Penicillamine (administration & dosage)</term>
<term>Penicillamine (adverse effects)</term>
<term>Rhabdomyolysis (etiology)</term>
<term>Stiffness</term>
<term>Sulfur containing aminoacid</term>
<term>Syndrome</term>
<term>Toxicity</term>
<term>Wilson disease</term>
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<term>Penicillamine</term>
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<term>Penicillamine</term>
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<keywords scheme="MESH" qualifier="chemically induced" xml:lang="en"><term>Dystonia</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Dystonia</term>
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<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en"><term>Hepatolenticular Degeneration</term>
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<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Fatal Outcome</term>
<term>Humans</term>
<term>Male</term>
<term>Syndrome</term>
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<term>Dystonie</term>
<term>Enzymopathie</term>
<term>Etude cas</term>
<term>Généralisé</term>
<term>Homme</term>
<term>Pénicillamine</term>
<term>Rigidité</term>
<term>Toxicité</term>
<term>Wilson maladie</term>
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<front><div type="abstract" xml:lang="en">A 37‐year‐old man with Wilson's disease is described, in whom the introduction of penicillamine therapy was followed after 3.5 weeks by the development of the status dystonicus with a fatal outcome.</div>
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<name sortKey="Kosti, Vladimir S" sort="Kosti, Vladimir S" uniqKey="Kosti V" first="Vladimir S." last="Kosti">Vladimir S. Kosti</name>
<name sortKey="Pejovi, Sanja" sort="Pejovi, Sanja" uniqKey="Pejovi S" first="Sanja" last="Pejovi">Sanja Pejovi</name>
<name sortKey="Sterni, Nadezda" sort="Sterni, Nadezda" uniqKey="Sterni N" first="Nadežda" last="Šterni">Nadežda Šterni</name>
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